| 產(chǎn)品編號(hào) | IHC0695H |
| 英文名稱 | Human Dysferlin Ready-To-Use IHC Kit |
| 中文名稱 | 人Dysferlin蛋白即用型免疫組化試劑盒 |
| 別 名 | DYSF; FER1L1; LGMD2B; MMD1 |
| 適用樣品基質(zhì) | FFPE tissue |
| 保存條件 | Please store components at the temperatures indicated on the individual tube labels. The kit is stable for 6 months from the date of receipt. |
| 產(chǎn)品介紹 |
Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM. SWISS: O75923 Gene ID: 8291 |
| 產(chǎn)品圖片 |
Immunohistochemical analysis of paraffin embedded Human skeletal muscle tissue slide using IHC0695H (Human Dysferlin Kit).
|
